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Diastolic myocardial dysfunction and it's relationship with systolic myocardial dysfunction in primary endocardial fibroelastosis
Author(s): 
Pages: 284-286
Year: Issue:  4
Journal: JOURNAL OF SOUTHEAST UNIVERSITY(MEDICAL SCIENCE EDITION)

Keyword:  原发性心内膜弹力纤维增生症舒张功能障碍收缩功能障碍;
Abstract: 目的:探讨原发性心内膜弹力纤维增生症(EFE)患儿是否存在主动舒张功能障碍及其与收缩功能障碍的关系.方法:EFE患儿44例,正常对照组50例.超声常规测量左室舒张末内径(LVEDD)、左房内径(LAD)、左室射血分数(LVEF)、左室舒张末容积(LVEDV)、 E峰流速(E)、A峰流速(A)和左室等容舒张时间(IVRT).结果:仅有舒张功能障碍7例,收缩功能障碍和舒张功能障碍并存37例.主动舒张功能障碍,即IVRT≥65ms者17例,IVRT<65ms 27例,两组比较,前者LVEF高、LAD小、E低、A高和E/A大(P<0.05).IVRT≥65ms时,控制变量LVEF情况下,即IVRT与LVEDD呈正相关(P<0.05),未发现LVEF与E/A或E相关(P>0.05).以IVRT 70ms为分界点分成两组,IVRT≥70ms组较<70ms组LVEDD大(P<0.05),而LVEF无显著差异.结论:EFE存在主动舒张功能障碍,随着舒张功能障碍加重,收缩功能下降加剧.
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