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Report of 8 Cases with POEMS Syndrome
Author(s): 
Pages: 227-229
Year: Issue:  4
Journal: CHINESE JOURNAL OF NEUROIMMUNOLOGY AND NEUROLOGY

Keyword:  POEMS综合征临床特征治疗;
Abstract: 目的描述POEMS综合征的临床特点,以提高对此病的认识.方法报道8例POEMS综合征患者临床表现、实验室检查及治疗方法并复习有关文献.结果8例患者均有周围神经病变,其中4例患者血有M-蛋白,症状复杂多样.对8例患者进行不同尝试的治疗,结果症状有一定改善.结论POEMS综合征是一少见的多系统损害疾病,发病机制不很清楚,常有多发性神经病、脏器肿大、内分泌病、M-蛋白和皮肤改变症状.早期病例易被误诊,临床应认真分析、检查,以提高临床检出率.
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